Journal article
Two-to-one AV block associated with the congenital long QT syndrome.
- Pruvot E Division of Cardiology, University Hospital, Lausanne, Switzerland. etienne.pruvot@hospvd.ch
- De Torrente A
- De Ferrari GM
- Schwartz PJ
- Goy JJ
- 1999-02-04
Published in:
- Journal of cardiovascular electrophysiology. - 1999
Adolescent
Cardiac Pacing, Artificial
Electrocardiography
Female
Follow-Up Studies
Heart Block
Humans
Long QT Syndrome
Purkinje Fibers
Sympathectomy
English
INTRODUCTION
Conduction abnormalities associated with long QT syndrome (LQTS) have been reported as "pseudo 2:1 AV block" due to sinus intervals shorter than ventricular refractoriness.
METHOD AND RESULTS
We report the electrophysiologic characteristics of a patient suffering from congenital LQTS with episodes of true 2:1 AV block. Induction of 2:1 infra-Hisian blocks and return to 1:1 conduction were observed using single atrial and ventricular extrastimuli. The block was located in the Purkinje network but not in the myocardium.
CONCLUSION
The His-Purkinje system of our LQTS patient displayed dynamic properties with a strong increase in refractoriness for short-long sequences and a decrease for long-short sequences that triggered intermittent 2:1 AV blocks.
Conduction abnormalities associated with long QT syndrome (LQTS) have been reported as "pseudo 2:1 AV block" due to sinus intervals shorter than ventricular refractoriness.
METHOD AND RESULTS
We report the electrophysiologic characteristics of a patient suffering from congenital LQTS with episodes of true 2:1 AV block. Induction of 2:1 infra-Hisian blocks and return to 1:1 conduction were observed using single atrial and ventricular extrastimuli. The block was located in the Purkinje network but not in the myocardium.
CONCLUSION
The His-Purkinje system of our LQTS patient displayed dynamic properties with a strong increase in refractoriness for short-long sequences and a decrease for long-short sequences that triggered intermittent 2:1 AV blocks.
- Language
-
- English
- Open access status
- closed
- Identifiers
-
- DOI 10.1111/j.1540-8167.1999.tb00647.x
- PMID 9930915
- Persistent URL
- https://folia.unifr.ch/global/documents/130665
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